{"id":13862,"date":"2019-10-11T20:33:45","date_gmt":"2019-10-11T20:33:45","guid":{"rendered":"https:\/\/sbpt.org.br\/portal\/?p=13862"},"modified":"2019-10-11T20:33:45","modified_gmt":"2019-10-11T20:33:45","slug":"doenca-intersticial-pulmonar-jbp","status":"publish","type":"post","link":"https:\/\/sbpt.org.br\/portal\/doenca-intersticial-pulmonar-jbp\/","title":{"rendered":"JBP publica artigo sobre doen\u00e7a intersticial pulmonar familiar"},"content":{"rendered":"<p style=\"text-align: justify\">H\u00e1 sugest\u00f5es que at\u00e9 20% das PIF possam ser de cunho familiar. A edi\u00e7\u00e3o do Jornal Brasileiro de Pneumologia volume 45, n. 5, traz o artigo &#8220;<a href=\"http:\/\/www.jornaldepneumologia.com.br\/detalhe_artigo.asp?id=2995\" target=\"_blank\" rel=\"noopener\">Fibrose pulmonar familiar: um espectro heterog\u00eaneo de apresenta\u00e7\u00f5es<\/a>&#8220;.<\/p>\n<p>Na pesquisa de Hortense et al<a href=\"http:\/\/www.jornaldepneumologia.com.br\/detalhe_artigo.asp?id=2995\" target=\"_blank\" rel=\"noopener\">\u00b9<\/a>,&nbsp;rec\u00e9m publicada no JBP, foram descritas as caracter\u00edsticas cl\u00ednicas de 35 casos \u00edndice de FPF, avaliados entre 2014 e 2017 no Brasil.<\/p>\n<h6>Fibrose Pulmonar Familiar<\/h6>\n<p style=\"text-align: justify\">A fibrose pulmonar familiar (FPF) \u00e9 definida como a ocorr\u00eancia de pelo menos dois casos de algum tipo de pneumonia intersticial fibrosante (PIF) em membros de uma mesma fam\u00edlia biol\u00f3gica.<\/p>\n<p style=\"text-align: justify\">A mediana da idade do diagn\u00f3stico foi elevada (66 anos) e n\u00e3o houve predom\u00ednio de sexo. Hist\u00f3ria de tabagismo e exposi\u00e7\u00e3o ambiental, em especial a aves, foi muito comum (45% e 80% dos casos).<\/p>\n<h6>Achados<\/h6>\n<p style=\"text-align: justify\">Os padr\u00f5es tomogr\u00e1ficos encontrados foram bastante heterog\u00eaneos, incluindo pneumonia intersticial n\u00e3o espec\u00edfica (26%) e pneumonia de hipersensibilidade cr\u00f4nica (2%). O padr\u00e3o tomogr\u00e1fico de pneumonia intersticial usual s\u00f3 foi detectado em 17% dos casos. Somente 4% dos pacientes mostraram evid\u00eancias sugestivas de telomeropatias.<\/p>\n<p style=\"text-align: justify\">De seis pacientes em que foram realizadas bi\u00f3psias pulmonares, a pneumonite de hipersensibilidade cr\u00f4nica foi diagnosticada em quatro.<\/p>\n<h6>Conclus\u00f5es<\/h6>\n<p style=\"text-align: justify\">De acordo com o Dr. Jos\u00e9 Ant\u00f4nio Baddini-Martinez, um dos autores do estudo, &#8220;\u00e9 importante investigar antecedentes familiares nos pacientes com suspeita de doen\u00e7a intersticial pulmonar&#8221;.<\/p>\n<p style=\"text-align: justify\">&#8220;Al\u00e9m disso, familiares de pacientes com FPF devem ter cuidado especial de n\u00e3o se expor a agentes possivelmente nocivos \u00e0 respira\u00e7\u00e3o, em especial tabagismo e cria\u00e7\u00e3o de aves&#8221;, explica.<\/p>\n<p style=\"text-align: justify\">&#8220;Finalmente, os pneumologistas devem estar cientes que FPF pode englobar uma heterogeneidade de apresenta\u00e7\u00f5es radiol\u00f3gicas e histol\u00f3gicas. Infelizmente, as d\u00favidas relacionadas com a melhor condu\u00e7\u00e3o cl\u00ednica nesses casos ainda s\u00e3o substanciais&#8221;.<\/p>\n<hr>\n<p style=\"text-align: justify\"><a href=\"http:\/\/www.jornaldepneumologia.com.br\/detalhe_artigo.asp?id=2995\" target=\"_blank\" rel=\"noopener\">\u00b9<\/a>Hortense AB, Santos MKD, Wada D, Fabro AT, Lima M, Rodrigues S, Calado RT, Baddini-Martinez J. Familial pulmonary fibrosis: a heterogeneous spectrum of presentations. J Bras Pneumol. 2019 Jun 10;45(5):e20180079. doi: 10.1590\/1806-3713\/e20180079.<\/p>\n<!-- AddThis Advanced Settings generic via filter on the_content --><!-- AddThis Share Buttons generic via filter on the_content -->","protected":false},"excerpt":{"rendered":"<p>H\u00e1 sugest\u00f5es que at\u00e9 20% das PIF possam ser de cunho familiar. A edi\u00e7\u00e3o do Jornal Brasileiro de Pneumologia volume 45, n. 5, traz o artigo &#8220;Fibrose pulmonar familiar: um espectro heterog\u00eaneo de apresenta\u00e7\u00f5es&#8220;. Na pesquisa de Hortense et al\u00b9,&nbsp;rec\u00e9m publicada no JBP, foram descritas as caracter\u00edsticas cl\u00ednicas de 35 casos \u00edndice de FPF, avaliados [&hellip;]<!-- AddThis Advanced Settings generic via filter on get_the_excerpt --><!-- AddThis Share Buttons generic via filter on get_the_excerpt --><\/p>\n","protected":false},"author":3,"featured_media":11978,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"ngg_post_thumbnail":0,"footnotes":""},"categories":[68],"tags":[92,581,84,299,85,697,698,699,179,180,700,98,701,549],"class_list":["post-13862","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-noticias","tag-dip","tag-doenca-intersticial","tag-doencas-intersticiais","tag-dpi","tag-fibrose-pulmonar","tag-fibrose-pulmonar-familiar","tag-fpf","tag-interstitial-lung-disease","tag-jbp","tag-jornal-brasileiro-de-pneumologia","tag-pif","tag-pneumonia","tag-pneumonia-intersticial","tag-pneumonite-de-hipersensibilidade"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.6 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>JBP publica artigo sobre doen\u00e7a intersticial pulmonar familiar<\/title>\n<meta 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